Q85.01 Neurofibromatosis, type 1
Instructional Notes:
-
Q85.01
Description: Neurofibromatosis, type 1
Inclusion Term:
- Von Recklinghausen disease
↓
-
Q85.0
Description: Neurofibromatosis (nonmalignant)
↓
-
Q85
Description: Phakomatoses, not elsewhere classified
Exclude1:
- ataxia telangiectasia [Louis-Bar] (G11.3)
- familial dysautonomia [Riley-Day] (G90.1)
↓
-
Q80-Q89
Description: Other congenital malformations (Q80-Q89)
↓
-
Q00-Q99
Description: Congenital malformations, deformations and chromosomal abnormalities
Exclude2:
- inborn errors of metabolism (E70-E88)
Notes:
- Codes from this chapter are not for use on maternal records